What does ECH mean in UNCLASSIFIED
Enoyl CoA Hydratase (ECH) is an abbreviation used in the field of biochemistry. It refers to an enzyme that catalyzes the hydration of enoyl-CoA intermediates in various metabolic pathways.
ECH meaning in Unclassified in Miscellaneous
ECH mostly used in an acronym Unclassified in Category Miscellaneous that means Enoyl CoA Hydratease
Shorthand: ECH,
Full Form: Enoyl CoA Hydratease
For more information of "Enoyl CoA Hydratease", see the section below.
Function of ECH
ECH plays a crucial role in the metabolism of fatty acids, branched-chain amino acids, and other molecules. It converts enoyl-CoA intermediates into their corresponding 3-hydroxyacyl-CoA derivatives, which are further processed in subsequent metabolic reactions.
ECH is involved in several metabolic pathways, including:
- Fatty acid beta-oxidation: In this pathway, ECH catalyzes the hydration of double bonds in fatty acyl-CoA molecules, allowing them to be further oxidized and broken down for energy production.
- Branched-chain amino acid degradation: ECH is involved in the degradation of certain branched-chain amino acids, such as leucine, isoleucine, and valine.
- Other pathways: ECH is also found in other metabolic pathways, such as the metabolism of prostaglandins and leukotrienes.
Essential Questions and Answers on Enoyl CoA Hydratease in "MISCELLANEOUS»UNFILED"
What is Enoyl CoA Hydratase (ECH)?
Enoyl CoA hydratase (ECH) is an enzyme involved in fatty acid metabolism. It catalyzes the addition of a water molecule to the double bond of enoyl-CoA intermediates, resulting in the formation of D-3-hydroxyacyl-CoA. This step is crucial in the beta-oxidation of fatty acids, which is the process by which the body breaks down fatty acids for energy production.
What is the role of ECH in beta-oxidation?
In beta-oxidation, ECH plays a vital role in converting enoyl-CoA into D-3-hydroxyacyl-CoA. This hydration reaction is essential for the subsequent steps of beta-oxidation, which involve the removal of two carbon atoms from the fatty acid chain.
What are the consequences of ECH deficiency?
ECH deficiency is a rare genetic disorder that leads to the accumulation of enoyl-CoA intermediates. This can disrupt fatty acid metabolism and cause a range of health problems, including metabolic acidosis, muscle weakness, and developmental delays.
How can ECH deficiency be treated?
Treatment for ECH deficiency typically involves a combination of dietary interventions and medications. The diet should be low in long-chain fatty acids and supplemented with medium-chain triglycerides, which are more easily metabolized. Medications, such as riboflavin and carnitine, may also be used to support energy production and reduce the accumulation of toxic metabolites.
What are the long-term effects of ECH deficiency?
The long-term effects of ECH deficiency can vary depending on the severity of the condition. With proper treatment and management, individuals with ECH deficiency can live relatively normal lives. However, they may experience ongoing challenges, such as growth retardation, muscle weakness, and learning difficulties.
Final Words: Enoyl CoA Hydratase (ECH) is a key enzyme in various metabolic pathways. It catalyzes the hydration of enoyl-CoA intermediates, facilitating the further metabolism of fatty acids, branched-chain amino acids, and other molecules. Understanding the function of ECH is essential for comprehending the complexities of cellular metabolism.
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